Malignant peripheral nerve sheath tumor with and without neurofibromatosis type 1
نویسندگان
چکیده
منابع مشابه
Malignant peripheral nerve sheath tumor with and without neurofibromatosis type 1.
Objective In this study, we review the institution's experience in treating malignant peripheral nerve sheath tumors (MPNSTs). A secondary aim was to compare outcomes between MPNSTs with and without neurofibromatosis type 1 (NF1). Methods Ninety-two patients with MPNSTs, over a period of 20 years, were reviewed. A retrospective chart review was performed. The median age was 43.5 years (range,...
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Malignant peripheral nerve sheath tumor (MPNST) is a rare soft tissue malignancy usually found in patients with neurofibromatosis type 1 (NF1) with a poor outcome. Although MPNST can be found in any part of the body including head and neck or extremities, intrathoracic MPNST with or without NF1 is uncommon, especially in children or adolescents. Reported herein is a case of huge intrathoracic M...
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ژورنال
عنوان ژورنال: Arquivos de Neuro-Psiquiatria
سال: 2017
ISSN: 0004-282X
DOI: 10.1590/0004-282x20170052